aTTP is acquired thrombotic thrombocytopenic purpura, and is also known as immune-mediated thrombotic thrombocytopenic purpura (iTTP). aTTP and iTTP are the same condition. Your healthcare team may use either term.

    The words that make up aTTP/iTTP help explain what is happening in the body.

    Acquired means you were not born with the condition. It is something you developed later in life. The main cause is not known. Immune-mediated means the cause of the condition is not known, but it happens when the immune system isn’t working normally.

    Thrombotic means blood clots form in the blood vessels. In aTTP/iTTP, small blood clots can form throughout the body.

    Thrombocytopenic means having a lower number of blood platelets than you should. This happens because the platelets clump together to make blood clots throughout the body.

    Purpura are purple bruises that are caused by bleeding under your skin. These bruises are a key symptom of aTTP/iTTP.

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about aTTP/iTTP >

    You may hear the term TTP used by your care team. TTP includes both acquired/immune-mediated TTP and hereditary or congenital TTP. Hereditary or congenital TTP is a condition people are born with that is extremely rare. Fewer than 5% of cases are hereditary.

    aTTP is also known as immune-mediated thrombotic thrombocytopenic purpura (iTTP). aTTP and iTTP are the same condition. Your healthcare team may use either term.

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura; TTP=thrombotic thrombocytopenic purpura.

    Learn more about aTTP/iTTP >

    Symptoms of an aTTP/iTTP episode can include:

    • Bleeding from the gums or nose
    • Purple bruises (known as purpura) and/or red or purple dots (known as petechiae) on the skin
    • Blood in urine
    • Stomach pain
    • Chest pain
    • Seizures
    • Headaches, confusion, or distorted vision
    • Tiredness and jaundice (a yellowing of the skin and eyes)

    If you think you are showing signs of an aTTP/iTTP episode, talk to your doctor or visit your local emergency room right away.

    aTTP/iTTP acquired/immune-mediated thrombotic thrombocytopenic purpura.

    aTTP/iTTP causes 3 things to go wrong in the body

    Autoantibody attacking ADAMTS13

    1

    The immune system attacks
    ADAMTS13 with autoantibodies

    What it means for the body

    If ADAMTS13 is being attacked, there won’t be enough in the blood

    Large vWF strand that ADAMTS13 can't cut

    2

    Because there is not enough
    ADAMTS13, vWF strands don’t get cut

    What it means for the body

    When vWF strands grow too long, they attract a lot of platelets when they are not supposed to, which means there are not enough platelets circulating in the blood

    Blood clot made from platelets sticking to large vWF strands

    3

    When long strands of vWF attract
    platelets, dangerous blood clots form in small blood vessels

    What it means for the body

    These blood clots can cause serious health problems like stroke, heart attack, seizures, and organ damage

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura; vWF=von Willebrand factor.

    Learn more about the signs of aTTP/iTTP >

    It’s not fully understood why some people develop aTTP/iTTP—it can affect anyone. 

    <2000 people
    aTTP/iTTP affects fewer than 2000 people in the United States every year.

    30 to 50 years old
    aTTP/iTTP usually affects people 30 to 50 years of age, but it can affect people of any age.

    Women
    aTTP/iTTP is more common in women than men.

    Black ethnicity
    aTTP/iTTP is more likely to affect people of Black ethnicity.

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about aTTP/iTTP >

    Diagnosis is normally made from a combination of medical history, physical examination, and laboratory tests.

    • Physical examinations may show some of the common symptoms of aTTP/iTTP, such as purple bruises (known as purpura) and/or red or purple dots (known as petechiae) on the skin, blood in urine, headaches, confusion, or distorted vision
    • Diagnostic tests to evaluate platelet and red blood cell count, ADAMTS13 enzyme activity levels, and organ function

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about aTTP/iTTP >

    Your doctor may perform certain lab tests to monitor your health at diagnosis and throughout an aTTP/iTTP episode.

    Platelets icon

    Platelet and red blood cell count

    Your doctor will confirm if you have fewer platelets and red blood cells than you should and if they are improving with treatment

    Low ADAMTS13 enzyme activity levels icon

    ADAMTS13 enzyme activity levels

    Your doctor will see how well your ADAMTS13 is working. Low levels mean aTTP/iTTP is active. Low levels can still occur during treatment and after other symptoms improve

    Warning icon

    Organ function

    Because clots can impact the organs, your doctor may perform different tests to check how well your organs are working

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    The goal of treatment is to address each problem aTTP/iTTP causes in the body.

    Immunosuppressive therapy icon

    Problem caused by aTTP/iTTP

    Your immune system attacks ADAMTS13 with autoantibodies
     

    Treatment

    Immunosuppressive therapy is a type of medicine that helps decrease the activity of your immune system. In aTTP/iTTP, it suppresses the production of anti-ADAMTS13 autoantibodies

    Plasma exchange icon

    Problem caused by aTTP/iTTP

    Because there is not enough ADAMTS13, von Willebrand factor (vWF) strands don’t get cut. When vWF strands grow too long, they attract a lot of platelets when they are not supposed to, which means there are not enough platelets circulating in the blood
     

    Treatment

    Plasma exchange (PEX) is a procedure that removes and replaces a person’s blood plasma over a few hours. In aTTP/iTTP, it replaces platelets and ADAMTS13 in the blood. PEX may need to be done for several days or weeks

    CABLIVI (caplacizumab-yhdp) treatment icon

    Problem caused by aTTP/iTTP

    When long strands of vWF attract platelets, dangerous blood clots may form when you don’t need them
     

    Treatment

    CABLIVI is a prescription medicine for adults, in combination with PEX and immunosuppression, designed specifically for aTTP/iTTP. It helps stop platelets from sticking to vWF and helps prevent your body from forming dangerous blood clots during an aTTP/iTTP episode

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura; vWF=von Willebrand factor.

    Learn more about aTTP/iTTP treatment >

    Acquired/immune-mediated thrombotic thrombocytopenic purpura (aTTP/iTTP) is a chronic condition that can have emergency episodes. You won’t need to take treatment every day for aTTP/iTTP forever. But after having 1 episode, it is possible to have another aTTP/iTTP episode. This is called a recurrence or a relapse. While some people may only experience 1 aTTP/iTTP episode, many others may experience a relapse. This means they may have another sudden aTTP/iTTP episode that requires therapy immediately.

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about living with aTTP/iTTP >

    Symptoms of an aTTP/iTTP recurrence are likely to be similar to an initial episode which can include:

    • Bleeding from the gums or nose
    • Purple bruises (known as purpura) and/or red or purple dots (known as petechiae) on the skin
    • Blood in urine
    • Stomach pain
    • Chest pain
    • Seizures
    • Headaches, confusion, or distorted vision
    • Tiredness and jaundice (a yellowing of the skin and eyes)

    If you think you are showing signs of an aTTP/iTTP episode, talk to your doctor or visit your local emergency room right away.

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about living with aTTP/iTTP >

    CABLIVI is a prescription treatment used to treat adults with acquired/immune-mediated thrombotic thrombocytopenic purpura (aTTP/iTTP*) designed to work with a procedure called plasma exchange and a medication called immunosuppressive therapy. CABLIVI, together with plasma exchange and immunosuppressive therapy, addresses each problem aTTP/iTTP causes in the body.

    *aTTP is also known as iTTP. You and your healthcare team can use either term.

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about CABLIVI >

    CABLIVI is a prescription treatment used to treat adults with acquired/immune-mediated thrombotic thrombocytopenic purpura (aTTP/iTTP*), with plasma exchange and immunosuppressive therapy.

    *aTTP is also known as iTTP. You and your healthcare team can use either term.

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about CABLIVI >

    CABLIVI is used together with a procedure called plasma exchange and a medication called immunosuppressive therapy to treat acquired/immune-mediated thrombotic thrombocytopenic purpura (aTTP/iTTP) in adults. CABLIVI has an active ingredient called caplacizumab-yhdp (cap-luh-siz-uh-mab). It is a small protein that is meant to prevent the body from forming dangerous blood clots during an aTTP/iTTP episode.

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about how CABLIVI works >

    It is recommended to inject CABLIVI every day you receive plasma exchange and for 30 days after your last plasma exchange session. Your doctor may decide you need to inject CABLIVI for more than 30 days. This additional period may last up to 28 days.

    Learn more about taking CABLIVI >

    DAY 1

    You will receive 2 doses of CABLIVI on day 1

    First dose: Your care team will give the first dose of CABLIVI through an IV injection before your first plasma exchange session

    Second dose: Your care team will give the second dose of CABLIVI as an injection into the skin of your stomach after your first plasma exchange session

    HOSPITAL STAY
    (number of days can vary)

    Every day after day 1, CABLIVI will be given after each plasma exchange session as an injection into the skin of your stomach

    Each person receives plasma exchange sessions for a different number of days. Your doctor will decide how many plasma exchange sessions you need

    After plasma exchange is no longer needed, you will continue to receive a CABLIVI injection into the skin of your stomach daily for the remainder of your stay and prepare to inject CABLIVI at home

    When your doctor decides you can safely leave the hospital, you will inject CABLIVI at home until it’s been 30 days since your last plasma exchange. Some people may need to inject CABLIVI longer (up to another 28 days), depending on their doctor’s direction.

    Your CABLIVI injection can be done by you, a family member, or another caregiver. Before you leave the hospital, you and your doctor should decide who that person will be. Your care team should teach you, your family, or your caregiver how to inject CABLIVI with confidence. Let your doctor know if you, your family, or your caregiver are not comfortable or if you have any questions.

    Learn more about taking CABLIVI >

    CABLIVI can cause side effects, although not everyone will experience them. Because CABLIVI works by stopping blood clots from forming, it may affect normal blood clotting and increase the risk of severe bleeding.

    In clinical studies, severe bleeding adverse reactions of nosebleed, bleeding from the gums, bleeding in the stomach or intestines, and bleeding from the uterus were each reported in 1% of people.

    Learn more about possible side effects of CABLIVI >

    With CABLIVI Patient Solutions, support is available to cover the cost of CABLIVI’s co-pay or co-insurance for qualified, commercially insured patients, up to the program maximum.* CABLIVI will be provided at no cost to eligible underinsured or uninsured patients.

    *Not valid for CABLIVI prescriptions covered by or submitted for reimbursement under Medicare, Medicaid, VA, DoD, Tricare, or similar federal or state programs including any state pharmaceutical assistance programs. Not valid where prohibited by law. Savings may vary depending on the patient’s out-of-pocket costs. Upon registration, the patient will receive all program details.
    Approval is not guaranteed. Sanofi reserves the right to modify or discontinue the programs at any time without notice.

    Learn more about patient assistance >

    Every insurance plan is different, so you will need to contact your insurance company to learn about your coverage options.

    With CABLIVI Patient Solutions, support is available to cover the cost of CABLIVI’s co-pay or co-insurance for qualified, commercially insured patients, up to the program maximum.* CABLIVI will be provided at no cost to eligible underinsured or uninsured patients.

    *Not valid for CABLIVI prescriptions covered by or submitted for reimbursement under Medicare, Medicaid, VA, DoD, Tricare, or similar federal or state programs including any state pharmaceutical assistance programs. Not valid where prohibited by law. Savings may vary depending on the patient’s out-of-pocket costs. Upon registration, the patient will receive all program details.
    Approval is not guaranteed. Sanofi reserves the right to modify or discontinue the programs at any time without notice.

    Learn more about patient assistance >

    You can receive additional education and resources in 2 ways:

    1. Enroll in CABLIVI Patient Solutions to be connected with a dedicated team that will work together seamlessly to help manage your aTTP/iTTP care.
    2. Fill out our sign-up form to stay informed about CABLIVI and aTTP/iTTP.

    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about patient assistance >

    For questions specific to your treatment and how you are doing, talk to your doctor.

    For questions about CABLIVI patient support services, CABLIVI Patient Solutions is available Monday through Friday, 8:00 AM to 8:00 PM ET, at 1-855-724-7222.

    Learn more about patient assistance >

    Taking CABLIVI once a day is important for successful treatment. However, if you miss a dose, do the following:

    • During your plasma exchange sessions: Inject CABLIVI as soon as possible
    • After you’re no longer on plasma exchange: Inject CABLIVI daily within 12 hours of your scheduled time. After 12 hours, skip the dose and inject the next scheduled dose

    You should inject only one (1) dose of CABLIVI at a time, as recommended by your doctor. If you have accidentally used more than this, don’t inject any more and call your doctor right away.
    Do not stop treatment early without talking with your doctor, even if you start to feel better. Stopping treatment too early may result in another aTTP/iTTP episode.


    aTTP/iTTP=acquired/immune-mediated thrombotic thrombocytopenic purpura.

    Learn more about taking CABLIVI >

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CABLIVI, in combination with PEX and immunosuppression, can help you take on aTTP/iTTP with confidence

IMPORTANT SAFETY INFORMATION AND INDICATIONS